A 47-year-old woman sought medical attention because of progressive disphagia for solids and liquids. She had lost 7 kilograms within the last three months. The physical examination was normal, except an enlarged and nodular thyroid gland. The patient's endoscopic, manometric, and barium swallow studies results were consistent with achalasia. She underwent fine needle aspiration biopsy (FNAB) due to a nodule in the right lobe of the thyroid gland and the cytological examination was reported as lymphocytic thyroiditis. There are few reports about achalasia and accompanying autoimmune thyroid diseases.