PRIMITIVE NEUROECTODERMAL TUMOR OF THE KIDNEY IN A CHILD

Citak E. C., Oguz A., KARADENİZ C., OKUR A., AKYÜREK N.

PEDIATRIC HEMATOLOGY AND ONCOLOGY, cilt.26, sa.7, ss.481-486, 2009 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 26 Sayı: 7
  • Basım Tarihi: 2009
  • Doi Numarası: 10.1080/08880010902754792
  • Dergi Adı: PEDIATRIC HEMATOLOGY AND ONCOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.481-486
  • Anahtar Kelimeler: children, primary renal PNET, EWS/FLI-1 FUSION TRANSCRIPTS, COOPERATIVE EWINGS-SARCOMA, DISTINCT ENTITY, BONE
  • Gazi Üniversitesi Adresli: Evet

Özet

Primary renal pimitive neuroectodermal tumor (PNET) is an extraordinarily rare neoplasm in childhood. It generally occurs in young adults and only a few pediatric cases have been reported. PNET in the kidney acts aggressively and the record shows poor therapeutic response. The authors present the case of a 16-year-old girl who was diagnosed with renal PNET and treated with high-dosage chemotherapy and peripheral blood stem cell transplantation (PBSCT).