Intrathoracic malignant peripheral nerve sheath tumor with angiosarcoma in a child with NF1

Elli, Murat; Can, Bilge; Ceyhan, Meltem; PINARLI, FARUK; Daǧdemir, Ayhan; Ayyildiz, Halil; Gürsel, Bilge; Daǧçinar, Adnan

doi:10.1177/030089160709300625

Intrathoracic malignant peripheral nerve sheath tumor with angiosarcoma in a child with NF1

Elli M., Can B., Ceyhan M., PINARLI F. G., Daǧdemir A., Ayyildiz H. S., ...Daha Fazla

Tumori, cilt.93, sa.6, ss.641-644, 2007 (SCI-Expanded, Scopus)

Yayın Türü: Makale / Tam Makale
Cilt numarası: 93 Sayı: 6
Basım Tarihi: 2007
Doi Numarası: 10.1177/030089160709300625
Dergi Adı: Tumori
Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
Sayfa Sayıları: ss.641-644
Gazi Üniversitesi Adresli: Evet

Özet

Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.