Portal Hypertensive Biliopathy as a Cause of Severe Cholestasis in Children With Congenital Hepatic Fibrosis

DALGIÇ A., SARI S., SÖZEN M. H., Kaya N. G., DALGIÇ B.

EXPERIMENTAL AND CLINICAL TRANSPLANTATION, vol.17, pp.223-225, 2019 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 17
  • Publication Date: 2019
  • Doi Number: 10.6002/ect.mesot2018.p79
  • Journal Name: EXPERIMENTAL AND CLINICAL TRANSPLANTATION
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.223-225
  • Keywords: Direct bilirubinemia, Icterus, Portal hypertension, VENOUS OBSTRUCTION
  • Gazi University Affiliated: Yes

Abstract

Portal hypertensive biliopathy may occur in patients with noncirrhotic hepatic fibrosis. Portal hypertensive biliopathy treatment should be focused on management of portal hypertension and relief of biliary obstruction. In patients with noncirrhotic portal fibrosis and symptomatic portal hypertensive biliopathy, portal decompression surgery by proximal splenorenal shunt is one successful treatment option.