Unexpected Progression of Tonsillar Herniation in Two Pediatric Cases with Chiari Malformation Type I and Review of the Literature

BÖRCEK A. Ö. , Aslan A.

PEDIATRIC NEUROSURGERY, vol.54, no.1, pp.51-56, 2019 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Review
  • Volume: 54 Issue: 1
  • Publication Date: 2019
  • Doi Number: 10.1159/000495066
  • Page Numbers: pp.51-56


Background: Chiari malformation type 1 (CM-1) is a generally congenital, rarely acquired disease characterized with 5 mm or more displacement of cerebellar tonsils through foramen magnum. Methods: Here, we report about 2 patients with CM-1 progressed in the degree of tonsillar herniation from our clinic, whereas increasing in prolapse of tonsillar herniation after diagnosis is extremely uncommon. Results: The first patient aged 17 years was diagnosed with CM-1 in 2009 and was operated due to progression of 5 mm radiologically and worsening symptoms in 2014. The second 5-month-old patient initially showed just low-settled tonsillar localization at the borderline, then it descended by 2 cm when the patient reached 3 years of age, yet could not be operated because of parents' objection. Conclusion: Due to lack of reports on increasing tonsillar descent in the literature, these case reports will contribute to natural history and management of CM-1. (c) 2018 S. Karger AG, Basel