A Rare Malign Tumor of The Lung; Low-Grade Fibromyxoid Sarcoma: Case Report


KURUL İ. C., ÇELİK A., AKYÜREK N., DEMİRÖZ Ş. M., DEMİRÖZ Ş. M., Memis L.

JOURNAL OF CLINICAL AND ANALYTICAL MEDICINE, sa.3, ss.356-358, 2012 (ESCI) identifier

  • Yayın Türü: Makale / Tam Makale
  • Basım Tarihi: 2012
  • Doi Numarası: 10.4328/jcam.546
  • Dergi Adı: JOURNAL OF CLINICAL AND ANALYTICAL MEDICINE
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.356-358
  • Gazi Üniversitesi Adresli: Evet

Özet

Primary sarcomas of lung are uncommon, and low-grade fibromyxoid sarcoma (LGFMS) located within the lung is exceedingly rare. We report an LGFMS arising from the lung in a 16-year old-girl. She was referred to our clinic for evaluation of the mass lesion found on left side of her chest rontgenogram. Surgical excision and lymph node dissection was performed via left thoracotomy. The microscopic appearance of the tumor exhibit bland fibroblastic spindle cells with a whorled or linear arrangement in fibrous and myxoid areas. The patient has remained well with no evidence of disease 2 years after. Although LGFMS has a deceptively benign histologic appearance, local recurrence and late metastases have frequently been reported. Low-grade fibromyxoid sarcoma is probably an underrecognized lung neoplasm and should be considered in the differential diagnosis of spindle cell neoplasms.