Airway management of a patient with Weill-Marchesani syndrome

Karabiyik L.

JOURNAL OF CLINICAL ANESTHESIA, cilt.15, sa.3, ss.214-216, 2003 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 15 Sayı: 3
  • Basım Tarihi: 2003
  • Doi Numarası: 10.1016/s0952-8180(02)00506-8
  • Dergi Adı: JOURNAL OF CLINICAL ANESTHESIA
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.214-216
  • Anahtar Kelimeler: Weill-Marchesani syndrome, difficult intubation, intubating, laryngeal mask, INTUBATING LARYNGEAL MASK, DIFFICULT INTUBATION
  • Gazi Üniversitesi Adresli: Evet

Özet

Weill-Marchesani syndrome is a genetically determined rare systemic connective tissue disorder consisting of brachymorphy, brachydactyly, aortic stenosis, and Ophthalmologic abnormalities, such as ectopia lentis, microspherophakia, and secondary glaucoma. The primary lesion is fibrous tissue hyperplasia. Airway control and intubation may be difficult in patients with WMS because of stiff joints, poorly aligned teeth, and maxillary hypoplasia with a narrow palate. We describe the successful airway management of a patient with WMS and laryngeal stenosis, using an intubating laryngeal mask following failed conventional laryngoscopic intubation. (C) 2003 by Elsevier Science Inc.