TURKISH JOURNAL OF PEDIATRICS, vol.38, no.2, pp.261-264, 1996 (SCI-Expanded)
Xeroderma pigmentosum (XP) is an autosomal recessive disorder characterized by severe sun-sensitivity, early skin cancers and abnormal DNA repair. XP has a worldwide distribution with an approximate frequency of 1/250,000. It Is classified into nine complementation groups, and distribution of patients among the various groups is related to ethnic origin.