Endomyocardial fibrosis causing right intraventricular gradient and obliteration

TAÇOY G., Tavli Y., ABACI A.

TURK KARDIYOLOJI DERNEGI ARSIVI-ARCHIVES OF THE TURKISH SOCIETY OF CARDIOLOGY, cilt.37, sa.6, ss.417-420, 2009 (ESCI) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 37 Sayı: 6
  • Basım Tarihi: 2009
  • Dergi Adı: TURK KARDIYOLOJI DERNEGI ARSIVI-ARCHIVES OF THE TURKISH SOCIETY OF CARDIOLOGY
  • Derginin Tarandığı İndeksler: Emerging Sources Citation Index (ESCI), Scopus, TR DİZİN (ULAKBİM)
  • Sayfa Sayıları: ss.417-420
  • Anahtar Kelimeler: Cardiomyopathy, restrictive, echocardiography, endomyocardial fibrosis, magnetic resonance imaging
  • Gazi Üniversitesi Adresli: Evet

Özet

Endomyocardial fibrosis is a cause of restrictive cardiomyopathy and it generally occurs in tropical regions more commonly affecting children and young adults. A 19 year old male patient presented with edema in the lower extremities and fatigue. Thransthoracic echocardiography showed dilated right heart chambers, restrictive physiology in the left ventricle, and increased tissue growth in the right ventricle which causes a 60 mmHg gradient and obliteration. Magnetic resonance imaging confirmed the presence of increased tissue formation in the right ventricular inflow region. Surgical resection was not considered taking into account the functional capacity of the patient (class II), disappearance of symptoms following medical treatment, and high risk for perioperative mortality. The presented case may arouse interest in that it increased tissue growth in the right ventricle, leading to an incorrect diagnosis, at another center, as idiopathic pulmonary hypertension.