Reports of malignant primary extradural ependymal tumours are exceptionally rare. We report the case of a 30-year-old woman who had an excision of a tumour in the subcutaneous sacrococcygeal region, as well as a right ilioinguinal dissection, 67 months prior to presenting with a mass at the same location. The tumor was excised again, preserving the coccyx. The diagnosis of sacrococcygeal anaplastic ependymoma was made. Eighteen months previously, the patient had been diagnosed as having malignant cystosarcoma phylloides in her right breast mass, which was treated with simple mastectomy. The diagnosis of phylloides was confirmed on re-evaluation of the pathological specimens, as well. An ependymoma with a phylloides tumor has not been previously reported in any patient. In this report, the computed tomography, clinical, and pathological features are discussed.