Acquired von Willebrand syndrome in a patient with Ewing sarcoma

Elli M., PINARLI F. G., Dagdemir A., Dabak N., Fisgin T., Selcuk M., ...Daha Fazla

PEDIATRIC HEMATOLOGY AND ONCOLOGY, cilt.23, sa.2, ss.111-114, 2006 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 23 Sayı: 2
  • Basım Tarihi: 2006
  • Doi Numarası: 10.1080/08880010500457749
  • Dergi Adı: PEDIATRIC HEMATOLOGY AND ONCOLOGY
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.111-114
  • Gazi Üniversitesi Adresli: Hayır

Özet

Acquired von Willebrand syndronze is a rare bleeding disorder with clinical and laboratory features closely resembling to hereditary von Willebrand disease. The syndrome may accompany various conditions, including malignant disorders, most often with Wilms tumor and adrenal cell carcinoma. In this report, the authors present a patient with AvWS in association with Ewing sarcoma for the first time in the literature. The abnormal bleeding tendency was successfully treated with fresh frozen plasma and did not recur after the first two courses of chemotherapy with clinical improvement.