SLEEP AND BREATHING, cilt.18, sa.1, ss.143-149, 2014 (SCI-Expanded)
Background Mucopolysaccharidoses (MPS) are a group of inherited lysosomal storage disorders caused by the deficiency of hydrolases involved in the degradative pathway of glycosaminoglycans. In MPS, upper airway obstruction may result from multiple causative factors which may impact severely upon morbidity and mortality.