PEDIATRIC RADIOLOGY, 2026 (SCI-Expanded, Scopus)
Immunoglobulin G4-related (IgG4-R) inflammatory pseudotumor of the ureter is a rare benign lesion that can closely mimic malignancy on imaging. We report a case of a 5-year-8-month-old boy who presented with hematuria. Ultrasound (US) examination demonstrated pelvicalyceal and ureteral dilatation and a ureteral mass lesion measuring 39 & times;18 mm. Unenhanced computed tomography (CT) and contrast-enhanced magnetic resonance imaging (MRI) demonstrated an intraluminal ureteral mass causing unilateral urinary tract dilatation. This case is unique due to its pediatric ureteral location and misleading clinical presentation. Recognizing the characteristic US and MRI features of ureteral IgG4-R inflammatory pseudotumor, along with careful consideration of intraluminal ureteral lesions in the setting of unexplained urinary tract dilatation, may help avoid delayed diagnosis, chronic obstructive uropathy, and unnecessary radical surgery.