Behcet's disease, originally described as a triad of orogenital ulcerations and uveitis, is a chronic, multisystem disorder involving the skin, mucous membranes, gastrointestinal tract, eyes, joints, central nervous system, and blood vessels. Vascular manifestations of Behcet's disease (vasculo-Behcet's disease) consists of venous and arterial forms. The arterial form is rare but carries a grave prognosis. The authors present a case of Behcet's disease that manifested itself with a rupture of an abdominal aortic aneurysm. The outcome, although successful in this case, poses a prognostic dilemma for the surgical team involved. The world literature in respect to complications and prognosis of vascular reconstruction in Behcet's disease is reviewed and discussed.