Extra-cardiac rhabdomyomas are rare benign soft tissue tumors accounting for 2% of sk eletal muscle neoplasms. Oral cavity and pharynx are the most common sites for rhabdomyomas origina ting from the head and neck region. The presenting symptom for head and neck rhabdomyomas may change according to tumor size and location. The main treatment modality is total surgical excision. In this study, we aimed to report an adult hypopharyngeal rhabdomyoma case presenting with dysphagia and globus sensation and to discuss head and neck extra-cardiac rhabdomyomas reported in the literature.