TURKISH JOURNAL OF PEDIATRICS, cilt.43, sa.4, ss.332-337, 2001 (SCI-Expanded)
In most instances, congenital arteriovenous fistula is only one manifestation of a more widespread abnormality; 60% of patients also have hereditary hemorrhagic telengiectasis (Rendu-Osler-Weber syndrome). Among those with congenital pulmonary arteriovenous fistula, the diagnosis is made during infancy in only 15% of patients.