Pulmonary arteriovenous fistula in the newborn - A case report of Rendu-Osler-Weber syndrome and a review of the literature
TURKISH JOURNAL OF PEDIATRICS, cilt.43, sa.4, ss.332-337, 2001 (SCI-Expanded, Scopus, TRDizin)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 43 Sayı: 4
- Basım Tarihi: 2001
- Dergi Adı: TURKISH JOURNAL OF PEDIATRICS
- Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, TR DİZİN (ULAKBİM)
- Sayfa Sayıları: ss.332-337
- Anahtar Kelimeler: arteriovenous fistula, Rendu-Osler-Weber syndrome, MALFORMATION, NEONATE
- Gazi Üniversitesi Adresli: Evet
Özet
In most instances, congenital arteriovenous fistula is only one manifestation of a more widespread abnormality; 60% of patients also have hereditary hemorrhagic telengiectasis (Rendu-Osler-Weber syndrome). Among those with congenital pulmonary arteriovenous fistula, the diagnosis is made during infancy in only 15% of patients.