UNUSUAL VARIATION OF ASPLENIA SYNDROME


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TUNAOGLU F., OLGUNTURK R., GUCUYENER K., DEMIRSOY S., UZAMIS C.

JAPANESE HEART JOURNAL, vol.32, no.6, pp.859-865, 1991 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 32 Issue: 6
  • Publication Date: 1991
  • Doi Number: 10.1536/ihj.32.859
  • Title of Journal : JAPANESE HEART JOURNAL
  • Page Numbers: pp.859-865

Abstract

The case of a 1-year-old cyanotic boy diagnosed with asplenia syndrome has been reported. By physical and laboratory examinations, levocardia, atrial inversion, primum ASD, single atrioventricular valve, single ventricle (left-hand morphology), rudimentary right ventricle (anterior, left-sided), pulmonary stenosis, left-sided vena cava, single vena cava superior were established and the case was diagnosed with asplenia syndrome. The patient has concordance between tracheo-bronchial situs and lung anatomy and inverted atrial and visceral situs, but without atrial isomerism that makes his case an unusual variation of asplenia syndrome.