Intrathoracic malignant peripheral nerve sheath tumor with angiosarcoma in a child with NF1


Elli M., Can B., Ceyhan M., PINARLI F. G. , Daǧdemir A., Ayyildiz H. S. , ...Daha Fazla

Tumori, cilt.93, sa.6, ss.641-644, 2007 (SCI Expanded İndekslerine Giren Dergi) identifier identifier

  • Cilt numarası: 93 Konu: 6
  • Basım Tarihi: 2007
  • Doi Numarası: 10.1177/030089160709300625
  • Dergi Adı: Tumori
  • Sayfa Sayıları: ss.641-644

Özet

Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.