Suspected familial odontogenic keratocysts related to Gorlin Goltz syndrome

Yucetas S., Cetiner S., Qygur T.

SAUDI MEDICAL JOURNAL, vol.27, no.2, pp.250-253, 2006 (SCI-Expanded) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 27 Issue: 2
  • Publication Date: 2006
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.250-253
  • Gazi University Affiliated: No


This report represents the suspected familial case series of odontogenic keratocysts (OKCs) related to Gorlin Goltz syndrome (GGS), a rare genetic disorder characterized mainly by multiple basal cell carcinomas, OKCs and other less frequent skeletal and neurological manifestations. Familial cases included grandmother's father, grandmother, father and son. Although they had all OKCs, father additionally possessed some of the other characteristics of GGS. We described all the patients' diagnoses, treatments and long-term follow-ups under the light of current literature.