Suspected familial odontogenic keratocysts related to Gorlin Goltz syndrome


Yucetas S., Cetiner S., Qygur T.

SAUDI MEDICAL JOURNAL, cilt.27, sa.2, ss.250-253, 2006 (SCI-Expanded) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 27 Sayı: 2
  • Basım Tarihi: 2006
  • Dergi Adı: SAUDI MEDICAL JOURNAL
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.250-253
  • Gazi Üniversitesi Adresli: Hayır

Özet

This report represents the suspected familial case series of odontogenic keratocysts (OKCs) related to Gorlin Goltz syndrome (GGS), a rare genetic disorder characterized mainly by multiple basal cell carcinomas, OKCs and other less frequent skeletal and neurological manifestations. Familial cases included grandmother's father, grandmother, father and son. Although they had all OKCs, father additionally possessed some of the other characteristics of GGS. We described all the patients' diagnoses, treatments and long-term follow-ups under the light of current literature.