Arterial embolisation and coiling for high-output heart failure and pulmonary hypertension A +/- nduced by hepatic arteriovenous fistula in a patient with hereditary hemorrhagic telengiectasia

Acikgoz S. K., Tacoy G., Onal B., Yildirim B., Cengel A.

CENTRAL EUROPEAN JOURNAL OF MEDICINE, cilt.4, sa.3, ss.369-373, 2009 (SCI-Expanded) identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 4 Sayı: 3
  • Basım Tarihi: 2009
  • Doi Numarası: 10.2478/s11536-009-0028-3
  • Dergi Adı: CENTRAL EUROPEAN JOURNAL OF MEDICINE
  • Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Sayfa Sayıları: ss.369-373
  • Anahtar Kelimeler: Hereditary hemorrhagic telengiectasia, Hepatic arterivenous fistula, Arterial embolisation, Coiling, WEBER-RENDU DISEASE, LIVER-DISEASE, TELANGIECTASIA, MALFORMATIONS
  • Gazi Üniversitesi Adresli: Evet

Özet

Hereditary hemorrhagic telangiectasia (HHT) is a genetic vascular disorder characterised by epistaxis, telangiectases, and visceral arteriovenous malformations. Hyperdynamic blood flow associated with arteriovenous malformations may lead to pulmonary hypertension, global heart failure, and valvular insufficiencies. We report a patient who had HHT with severe heart failure (New York Heart Association [NYHA] class III-IV) and pulmonary hypertension caused by an hepatic arteriovenous fistula. After successful transarterial embolisation of the right branch of the hepatic artery with polyvinyl alcohol (PVA) particles and coils, 4 to 7 mm in size, the patient was discharged with functional class II (NYHA) heart failure.