Hepatopulmonary Syndrome and Multiple Arteriovenous Fistulas in a Child with Niemann-Pick Disease


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Onay Z. R. , Ramaslı Gürsoy T. , Aslan A. T. , Şişmanlar Eyüboğlu T. , Akkan M. K.

PEDIATRIC ALLERGY IMMUNOLOGY AND PULMONOLOGY, cilt.34, sa.1, ss.30-32, 2021 (SCI İndekslerine Giren Dergi) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 34 Konu: 1
  • Basım Tarihi: 2021
  • Doi Numarası: 10.1089/ped.2020.1244
  • Dergi Adı: PEDIATRIC ALLERGY IMMUNOLOGY AND PULMONOLOGY
  • Sayfa Sayıları: ss.30-32

Özet

Background: Niemann-Pick disease (NPD) is caused by abnormal storage of sphingomyelin. NPD may affect the pulmonary system and cause hypoxia. In the present case, both hepatopulmonary syndrome (HPS) and pulmonary arteriovenous fistulas (PAVFs) developed in a child with NPD and were successfully treated with repeated embolization.