Hepatopulmonary Syndrome and Multiple Arteriovenous Fistulas in a Child with Niemann-Pick Disease.

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Onay Z. R., Ramaslı Gürsoy T., Aslan A. T., Şişmanlar Eyüboğlu T., Akkan M. K.

Pediatric allergy, immunology, and pulmonology, cilt.34, sa.1, ss.30-32, 2021 (SCI-Expanded, Scopus)

• Yayın Türü: Makale / Tam Makale
• Cilt numarası: 34 Sayı: 1
• Basım Tarihi: 2021
• Doi Numarası: 10.1089/ped.2020.1244
• Dergi Adı: Pediatric allergy, immunology, and pulmonology
• Derginin Tarandığı İndeksler: Science Citation Index Expanded (SCI-EXPANDED), Scopus, Academic Search Premier, BIOSIS, CAB Abstracts, CINAHL, EMBASE, MEDLINE, Veterinary Science Database
• Sayfa Sayıları: ss.30-32
• Açık Arşiv Koleksiyonu: AVESİS Açık Erişim Koleksiyonu
• Gazi Üniversitesi Adresli: Evet

Özet

Background: Niemann-Pick disease (NPD) is caused by abnormal storage of sphingomyelin. NPD may affect the pulmonary system and cause hypoxia. In the present case, both hepatopulmonary syndrome (HPS) and pulmonary arteriovenous fistulas (PAVFs) developed in a child with NPD and were successfully treated with repeated embolization.