Intrathoracic malignant peripheral nerve sheath tumor with angtosarcoma in a child with NF1

Elli M., Can B., Ceyhan M., PINARLI F. G., Dagdemir A., Ayyildiz H. S., ...More

TUMORI J, vol.93, no.6, pp.641-644, 2007 (SCI-Expanded) identifier

  • Publication Type: Article / Article
  • Volume: 93 Issue: 6
  • Publication Date: 2007
  • Journal Name: TUMORI J
  • Journal Indexes: Science Citation Index Expanded (SCI-EXPANDED), Scopus
  • Page Numbers: pp.641-644
  • Gazi University Affiliated: Yes


Malignant peripheral nerve sheath tumors (MPNSTs) are uncommon in children and adolescents but occur more frequently in NF1 patients. Angiosarcomatous differentiation in MPNSTs is a rare entity with poor prognosis. We report on a 13-year-old boy with intrathoracic angiosarcoma arising in MPNST associated with NF1.