Severe coronary artery disease in a 21-year-old girl with pseudoxanthoma elasticum and anomalous origin of the right coronary artery.

Kocaman S. A. , Tavil Y., Yalcin M. R.

Acta cardiologica, cilt.62, sa.4, ss.417-9, 2007 (SCI Expanded İndekslerine Giren Dergi) identifier identifier identifier

  • Yayın Türü: Makale / Tam Makale
  • Cilt numarası: 62 Konu: 4
  • Basım Tarihi: 2007
  • Doi Numarası: 10.2143/ac.62.4.2022288
  • Dergi Adı: Acta cardiologica
  • Sayfa Sayıları: ss.417-9


Pseucloxanthoma elasticum (PXE) is a genetic disorder characterized by progressive calcific degeneration and fragmentation of the elastic fibres. We present a patient with PXE who had premature atherosclerosis that had involved severely all major coronary vessels as well as an anomalous origin of right coronary artery.