Acta cardiologica, cilt.62, sa.4, ss.417-9, 2007 (SCI-Expanded)
Pseucloxanthoma elasticum (PXE) is a genetic disorder characterized by progressive calcific degeneration and fragmentation of the elastic fibres. We present a patient with PXE who had premature atherosclerosis that had involved severely all major coronary vessels as well as an anomalous origin of right coronary artery.