Polyarteritis nodosa in a case of familial Mediterranean fever

Bakkaloglu S., Muzac S., Akpek S., Soylemezoglu O., Buyan N., Hasanoglu E.

PEDIATRIC NEPHROLOGY, vol.19, no.5, pp.536-538, 2004 (Journal Indexed in SCI) identifier identifier identifier

  • Publication Type: Article / Article
  • Volume: 19 Issue: 5
  • Publication Date: 2004
  • Doi Number: 10.1007/s00467-003-1390-z
  • Title of Journal : PEDIATRIC NEPHROLOGY
  • Page Numbers: pp.536-538


We describe a 7-year-old boy with familial Mediterranean fever (FMF) complicated by polyarteritis nodosa (PAN) with distinct angiographic findings. On admission, he had abdominal pain, arthralgia, and severe fibromyalgia. During hospitalization, he displayed maculopapular eruptions, high blood pressure, gastrointestinal bleeding, and persistent constitutional symptoms mimicking a vasculitic process, most probably PAN. Renal angiography showed a perfusion defect compatible with a renal infarction secondary to a vasculitic process. He responded well to pulse methylprednisolone therapy with colchicine. We emphasize the rare association of IMF and PAN and the non-aneurysmal angiographic signs of PAN.