Kawasaki disease shock syndrome: Case report. Kawasaki hastaliǧi şok sendromu: Bir vaka takdimi
Cocuk Sagligi ve Hastaliklari Dergisi, cilt.59, sa.3, ss.131-135, 2016 (Scopus)
- Yayın Türü: Makale / Tam Makale
- Cilt numarası: 59 Sayı: 3
- Basım Tarihi: 2016
- Dergi Adı: Cocuk Sagligi ve Hastaliklari Dergisi
- Derginin Tarandığı İndeksler: Scopus
- Sayfa Sayıları: ss.131-135
- Anahtar Kelimeler: Kawasaki disease, Shock
- Gazi Üniversitesi Adresli: Evet
Özet
Kawasaki disease (KD) is a generalized systemic vasculitis predominantly involving medium-sized arteries. The Kawasaki disease shock syndrome (KDSS) was reported firstly as myocardial dysfunction, earlier onset, coronary artery involvement, and poor response to standard intravenous immunoglubulin (IVIG) therapy. A three-month-old girl was admitted with high fever, irritability, poor feeding and hemodynamic instability. For the presence of pyuria, fever and clinical sepsis suspicion, intravenous empirical antibiotic treatment was commenced with a preliminary diagnosis of urosepsis. Thereafter, an echocardiographic investigation was performed because of persistent fever and increasing platelet counts. Kawasaki disease was diagnosed by determining coronary artery dilation on echocardiography. Here, a young infant with KDSS was reported to emphasise this uncommon presentation of Kawasaki disease, because of possible fatal outcome without timely IVIG treatment.