Splenic hamartoma is a rarely diagnosed tumor in children. Most patients with splenic hamartomas are asymptomatic and a few have clinical findings. Most frequently reported symptoms include pancytopenia, anemia, and thrombocytopenia. Less commonly, fever, malaise, an weight loss have been reported. In the last decades, most of the splenic hamartomas were found incidentally during laparatomy or autopsy. The use of modern radiologic imaging techniques such as sonography, computed tomography, radionuclide scintigraphy, and magnetic resonance imaging showed that splenic hamartoma was not as uncommon as it was thought previously. We presented a 28-month-old girl who had a history of frequent infections, fever anemia. On the physical examination, she had a palpable mass in the left upper quadrant of her abdomen. The sonography and computed tomography revealed that she had a mass of 5 x 4 x 4 cm in the lower pole of her spleen first thought to be a splenic hamartoma. We excised the splenic mass by partial splenectomy. The histopathological findings were compatible with splenic hamartoma. The reported patient is the third case of symptomatic splenic hamartoma in the English treated with partial splenectomy. Despite numerous imaging modalities available, it is difficult to base the a definitive diagnosis of splenic hamartoma solely on imaging. It is often necessary to obtain a tissue diagnosis to eliminate the possibility of malignancy. Spleen has important hematologic and immunologic functions especially in children, therefore, spleen-preserving surgery is an acceptable and desirable principle in the treatment of benign splenic lesions.